However, late survival of unoperated adult patients with Ebstein anomaly is less than expected. The oldest patient at the Mayo Clinic to undergo primary operation was 79 years of age. Dearani, in Diagnosis and Management of Adult Congenital Heart Disease (Second Edition), 2011 Late OutcomeĮbstein anomaly may remain undetected until late childhood or adulthood. Whatever your care needs, we will put you in touch with specialists who can help.Morgan L. #EBSTEIN ANOMALY FREE#Please, feel free to contact us at 60 with any questions or request an appointment online. Velez believes that “by working together, we can help ensure every child has access to the life-changing or lifesaving cardiovascular care they need." Contact us The Heart Center team at Phoenix Children’s is more than willing to consult with providers in the Southwestern United States to share their experience and expertise. Congenital heart patients will be supported and guided as they transition from pediatric to adult care. Fortunately for patients who live in Arizona, Phoenix Children’s Heart Center is poised to provide the comprehensive care that is necessary across the lifespan through its Adult Congenital Heart Disease Program. It is important to note patients with Ebstein’s Anomaly will require lifelong monitoring and cardiovascular therapy to manage any and all lasting complications. Evidence has confirmed we can expect consistent results and long-term durability across all variations in tricuspid valve migration and dilation.” With you for the journey Velez, “We’ve reached the point where we can say with confidence that the cone reconstruction procedure is a safe and highly effective treatment for children with Ebstein’s Anomaly. Results indicated the cone reconstruction had a higher success rate and lower incidence of tricuspid regurgitation when compared to valve replacement or other surgical interventions. Specialists and surgeons have continued to analyze and refine the procedure, which has become the gold standard to treat Ebstein’s Anomaly.Ī retrospective study published in May 2020 in the Journal of Thoracic and Cardiovascular Surgery compared outcomes from 151 patients with Ebstein’s Anomaly. Since its initial unveiling, results of this autologous procedure have continued to show incredible promise with no chance of rejection. Cone reconstruction is possible at any age, however, when performed in children, the new valve continues to grow with the child. His groundbreaking surgical procedure involved using the patient’s own tissue to reconstruct the tricuspid valve through mobilization and rotation of the leaflets into a cone shape. Jose Pedro da Silva, a pediatric cardiovascular surgeon. History of the surgeryĪn alternative option was developed and first implemented in 1993 by Dr. Velez and his team have completed ten cone repairs since 2017 on patients ranging from neonates to adults. da Silva at the Children’s Hospital of Pittsburgh so that he could bring this life-saving service back to Phoenix Children’s. Velez, MD, received his formal surgical training from prominent cardiovascular programs around the world, but to master cone reconstruction, Dr. The Adult Congenital Heart Disease Program in Phoenix Children’s nationally ranked Heart Center now offers cone reconstruction surgery of the tricuspid valve as an alternative treatment for patients with congenital heart defects.Ĭhief of the Division of Cardiothoracic Surgery and Co-Director of the Phoenix Children’s Heart Center, Daniel A. Cone procedure offered at Phoenix Children’s provides hope While this surgery can alleviate symptoms, long-term outcomes have been poor because the patient either outgrows the valve or it degenerates, thereby prompting additional medical or surgical interventions. Traditional management of Ebstein’s Anomaly has involved tricuspid valve replacement. Without prompt treatment, life-threatening complications can occur including arrythmias, cyanosis and oxygenation issues, reduced physical activity, fluid accumulation, slower growth, and even heart failure. It is also typical of children diagnosed with Ebstein’s Anomaly to experience other cardiac abnormalities including septal defects or pulmonary valve stenosis. Ebstein's Anomaly, pre-surgery, showing severe tricuspid regurgitation Additional abnormalities
0 Comments
Leave a Reply. |
AuthorWrite something about yourself. No need to be fancy, just an overview. ArchivesCategories |